Pityriasis rubra pilaris

Pityriasis rubra pilaris
Pityriasis rubra pilaris
Classification and external resources
ICD-10 L44.0
ICD-9 696.4
OMIM 173200
DiseasesDB 29305
MedlinePlus 001471
eMedicine derm/337
MeSH D010916

Pityriasis rubra pilaris (also known as "Devergie's disease,"[1] "Lichen ruber acuminatus,"[1] and "Lichen ruber pilaris"[1]) refers to a group of chronic disorders characterized by reddish orange, scaling plaques and keratotic follicular papules.[2]:442 Symptoms may include reddish-orange patches (Latin: rubra) on the skin, severe flaking (Latin: pityriasis), uncomfortable itching, thickening of the skin on the feet and hands, and thickened bumps around hair follicles (Latin: pilus for hair). For some, early symptoms may also include generalized swelling of the legs, feet and other parts of the body. PRP has a varied clinical progression and a varied rate of improvement. There is no known cause or cure.[citation needed]

It was first described by Marie-Guillaume-Alphonse Devergie in 1856,[3] and the condition is also known as Devergie's disease.[4]



Dr. W.A.D. Griffiths, from Great Britain, classified six forms of PRP in the early 1980s.[5] At this time, the causes of PRP are still unknown and symptoms can be difficult to diagnose. Frequently, more than one medical professional will be consulted before an accurate PRP diagnosis is made.[citation needed]

Dermatologists have identified both an acquired form and an inherited form (familial) of PRP and have described them in medical journals. The acquired form usually shows a spontaneous or gradual remission of symptoms within several years although long-term symptoms may continue for years. The inherited form starts early in childhood with persistent long-term symptoms into adulthood.[citation needed]

Although most people who develop PRP are over age 50, individuals of any age, race, and nationality can be affected. Women and men seem to be equally affected.[citation needed]

See also


  1. ^ a b c Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0. 
  2. ^ Freedberg, et al. (2003). Fitzpatrick's Dermatology in General Medicine. (6th ed.). McGraw-Hill. ISBN 0071380760.
  3. ^ Devergie M. G. A. (1856). "[Pityriasis pilaris, a skin disease not described by dermatologists] (Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes)." (in French). Gazette hebdomadaire de médecine et de chirurgie, Paris 3: 197–201. 
  4. ^ M. G. A. Devergie and the eponymous named Devergie's disease at Who Named It?
  5. ^ "Pityriasis rubra pilaris". DermNZ (New Zealand Dermatological Society). 26 December 2006. http://dermnetnz.org/scaly/pityriasis-rubra-pilaris.html. Retrieved 2007-05-08.  - describes the various forms

External links

  • PRP Support Group - information regarding day-to-day care and medical treatment and having an international membership.
  • skin diseases Information
  • Dr. Griffith (June 1998). "Pityriasis rubra pilaris". In Editors Champion R.H., Burton J.L., Burns D.A. and Breathnach S.M.. Textbook of Dermatology. 2 (6th ed.). pp. 1539–1545. ISBN 0632050640. 

Wikimedia Foundation. 2010.

Игры ⚽ Нужно сделать НИР?

Look at other dictionaries:

  • Pityriasis rubra pilaris — Klassifikation nach ICD 10 L44.0 Pityriasis rubra pilaris …   Deutsch Wikipedia

  • pityriasis rubra pilaris — pityriasis ru·bra pi·lar·is rü brə pi lar əs n a chronic dermatitis characterized by the formation of papular horny plugs in the hair follicles and pinkish macules which tend to spread and become scaly plaques * * * a chronic, inflammatory,… …   Medical dictionary

  • Pityriasis rubra pilaris — Stachelflechte …   Universal-Lexikon

  • Pityriasis lichenoides et varioliformis acuta — Classification and external resources ICD 10 L41.0 …   Wikipedia

  • Pityriasis lichenoides chronica — Classification and external resources ICD 10 L41.1 ICD 9 696.2 …   Wikipedia

  • Pityriasis — (Griechisch πίτυρον Kleie) beschreibt die (Ab ) Schuppung der Haut. Klassifikation Unterformen Pityriasis alba Pityriasis lichenoides chronica Pityriasis lichenoides et varioliformis acuta Pityriasis rosea Pityriasis circinata Pityriasis rubra… …   Deutsch Wikipedia


  • rubra — see PITYRIASIS RUBRA PILARIS …   Medical dictionary

  • Pityriasis — Infobox Disease Name = Pityriasis Caption = DiseasesDB = ICD10 = ICD9 = ICD9|696.5 ICDO = OMIM = MedlinePlus = eMedicineSubj = eMedicineTopic = MeshID = D010915 Pityriasis commonly refers to flaking of the skin. Types include: * Pityriasis… …   Wikipedia

  • PITYRIASIS — (от греч. pityron отруби), со времени Виллана и Бейтмена (Willan, Bateman> морфологич. термин для обозначения стойкого мелкого отрубевидного шелушения, пятнистого или диффузного, на сухой (без мокнутия и корок) коже, то неизмененной в цвете и… …   Большая медицинская энциклопедия

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”