- Pityriasis rubra pilaris
Pityriasis rubra pilaris Classification and external resources ICD-10 L44.0 ICD-9 696.4 OMIM 173200 DiseasesDB 29305 MedlinePlus 001471 eMedicine derm/337 MeSH D010916
Pityriasis rubra pilaris (also known as "Devergie's disease," "Lichen ruber acuminatus," and "Lichen ruber pilaris") refers to a group of chronic disorders characterized by reddish orange, scaling plaques and keratotic follicular papules.:442 Symptoms may include reddish-orange patches (Latin: rubra) on the skin, severe flaking (Latin: pityriasis), uncomfortable itching, thickening of the skin on the feet and hands, and thickened bumps around hair follicles (Latin: pilus for hair). For some, early symptoms may also include generalized swelling of the legs, feet and other parts of the body. PRP has a varied clinical progression and a varied rate of improvement. There is no known cause or cure.
Dr. W.A.D. Griffiths, from Great Britain, classified six forms of PRP in the early 1980s. At this time, the causes of PRP are still unknown and symptoms can be difficult to diagnose. Frequently, more than one medical professional will be consulted before an accurate PRP diagnosis is made.
Dermatologists have identified both an acquired form and an inherited form (familial) of PRP and have described them in medical journals. The acquired form usually shows a spontaneous or gradual remission of symptoms within several years although long-term symptoms may continue for years. The inherited form starts early in childhood with persistent long-term symptoms into adulthood.
Although most people who develop PRP are over age 50, individuals of any age, race, and nationality can be affected. Women and men seem to be equally affected.
- List of cutaneous conditions
- American Osteopathic Dermatology content: http://www.aocd.org/skin/dermatologic_diseases/pityriasis_rubra_p.html
- ^ a b c Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
- ^ Freedberg, et al. (2003). Fitzpatrick's Dermatology in General Medicine. (6th ed.). McGraw-Hill. ISBN 0071380760.
- ^ Devergie M. G. A. (1856). "[Pityriasis pilaris, a skin disease not described by dermatologists] (Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes)." (in French). Gazette hebdomadaire de médecine et de chirurgie, Paris 3: 197–201.
- ^ M. G. A. Devergie and the eponymous named Devergie's disease at Who Named It?
- ^ "Pityriasis rubra pilaris". DermNZ (New Zealand Dermatological Society). 26 December 2006. http://dermnetnz.org/scaly/pityriasis-rubra-pilaris.html. Retrieved 2007-05-08. - describes the various forms
- PRP Support Group - information regarding day-to-day care and medical treatment and having an international membership.
- skin diseases Information
- Dr. Griffith (June 1998). "Pityriasis rubra pilaris". In Editors Champion R.H., Burton J.L., Burns D.A. and Breathnach S.M.. Textbook of Dermatology. 2 (6th ed.). pp. 1539–1545. ISBN 0632050640.
Diseases of the skin and appendages by morphology GrowthsPigmentedDermal and
PurpuraMacularthrombocytopenic purpura · actinic purpuraPapularIndurated
Papulosquamous disorders (L40–L45, 696–697) PsoriasisPustularGeneralized pustular psoriasis (Impetigo herpetiformis) · Acropustulosis/Pustulosis palmaris et plantaris (Pustular bacterid) · Annular pustular psoriasis · Localized pustular psoriasisOther Parapsoriasis Other pityriasisPityriasis rosea · Pityriasis rubra pilaris · Pityriasis rotunda · Pityriasis amiantacea Other lichenoid
configuration: Annular lichen planus · Linear lichen planus
morphology of lesion: Hypertrophic lichen planus · Atrophic lichen planus · Bullous lichen planus · Ulcerative lichen planus · Lichen planus actinicus · Lichen planus pigmentosussite of involvement: Mucosal lichen planus · Lichen planus of the nails · Peno-gingival syndrome · Vulvovaginal gingival syndrome
overlap: Lichen planus–lichen sclerosus overlap syndrome · Lichen planus–lupus erythematosus overlap syndromespecial forms: Hepatitis-associated lichen planus · Lichen planus pemphigoidesOtherLichen nitidus · Lichen striatus · Lichen ruber moniliformis · Gianotti–Crosti syndrome
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