Hearing impairment

See also: Deaf culture for the social movement..

Deaf and/or hard of hearing
Classification and external resources
The International Symbol for Deafness
ICD-10	H90-H91
ICD-9	389
DiseasesDB	19942
MeSH	D034381

Deafness is a condition wherein the ability to detect certain frequencies of sound is completely or partially impaired. When applied to humans, the term hearing impaired is rejected by the majority of deaf people where the terms deaf and hard-of-hearing are preferred.

Definition

Hearing sensitivity is indicated by the quietest sound that an animal can detect, called the hearing threshold. In the case of humans and some animals, this threshold can be accurately measured by a behavioral audiogram. A record is made of the quietest sound that consistently prompts a response from the listener. The test is carried out for sounds of different frequencies. There are also electro-physiological tests that can be performed without requiring a behavioral response.

Normal hearing thresholds within any given species are not the same for all frequencies. If different frequencies of sound are played at the same amplitude, some will be perceived as loud, and others quiet or even completely inaudible. Generally, if the gain or amplitude is increased, a sound is more likely to be perceived. Ordinarily, when animals use sound to communicate, hearing in that type of animal is most sensitive for the frequencies produced by calls, or in the case of humans, speech. All levels of the auditory system contribute to this sensitivity toward certain frequencies, from the outer ear's physical characteristics to the nerves and tracts that convey the nerve impulses of the auditory portion of the brain.

A hearing loss exists when an animal has diminished sensitivity to the sounds normally heard by its species. In humans, the term hearing impairment is usually reserved for people who have relative insensitivity to sound in the speech frequencies. The severity of a hearing loss is categorized according to the increase in volume that must be made above the usual level before the listener can detect it. In profound deafness, even the loudest sounds that can be produced by an audiometer (an instrument used to measure hearing) may not be detected.

Another aspect to hearing involves the perceived clarity of a sound rather than its amplitude. In humans, that aspect is usually measured by tests of speech perception. These tests measure one's ability to understand speech, not to merely detect sound. There are very rare types of hearing impairments which affect speech understanding alone.^[1]

Classification

Hearing impairments are categorized by their type (conductive, sensorineural, or both), by their severity, and by the age of onset. Furthermore, a hearing impairment may exist in only one ear (unilateral) or in both ears (bilateral).

Conductive and sensorineural hearing impairments

Main article: Conductive hearing loss

Main article: Sensorineural hearing loss

A conductive hearing impairment is an impairment resulting from dysfunction in any of the mechanisms that normally conduct sound waves through the outer ear, the eardrum or the bones of the middle ear.

A sensorineural hearing impairment is one resulting from dysfunction in the inner ear, especially the cochlea where sound vibrations are converted into neural signals, or in any part of the brain that subsequently processes these signals. The vast majority of human sensorineural hearing loss is associated with abnormalities in the hair cells of the organ of Corti in the cochlea. This dysfunction may be present from birth due to genetic or developmental abnormalities, or arise through trauma or disease during the lifetime of an individual. There are also very unusual sensorineural hearing impairments that involve the VIIIth cranial nerve, the Vestibulocochlear nerve or, in rare cases, auditory cortex. Damage to parts of the brain that process auditory signals can lead to a condition in which sounds may be heard at normal thresholds, but the quality of the sound perceived is so poor that speech cannot be understood. Sensorineural hearing loss associated with abnormalities of the auditory system in the brain is called Central Hearing Impairment.

Quantification of hearing loss

An audiologist conducting an audiometric hearing test in a sound-proof testing booth

The severity of a hearing impairment is ranked according to the additional intensity above a nominal threshold that a sound must be before being detected by an individual; it is (measured in decibels of hearing loss, or dB HL). Hearing impairment may be ranked as mild, moderate, moderately severe, severe or profound as defined below:

• Mild:
  • for adults: between 26 and 40 dB HL
  • for children: between 20 and 40 dB HL
• Moderate: between 41 and 55 dB HL
• Moderately severe: between 56 and 70 dB HL
• Severe: between 71 and 90 dB HL
• Profound: 91 dB HL or greater

Hearing sensitivity varies according to the frequency of sounds. To take this into account, hearing sensitivity can be measured for a range of frequencies and plotted on an audiogram.

For certain legal purposes such as insurance claims, hearing impairments are described in terms of percentages. Given that hearing impairments can vary by frequency and that audiograms are plotted with a logarithmic scale, the idea of a percentage of hearing loss is somewhat arbitrary, but where decibels of loss are converted via a recognized legal formula, it is possible to calculate a standardized "percentage of hearing loss" which is suitable for legal purposes only.

Another method for quantifying hearing impairments is a speech-in-noise test. As the name implies, a speech-in-noise test gives an indication of how well one can understand speech in a noisy environment. A person with a hearing loss will often be less able to understand speech, especially in noisy conditions. This is especially true for people who have a sensorineural loss – which is by far the most common type of hearing loss. As such, speech-in-noise tests can provide valuable information about a person's hearing ability, and can be used to detect the presence of a sensorineural hearing loss. A triple-digit speech-in-noise test was developed by RNID as part of a EU funded project Hearcom. The RNID version is available over the phone [phone], only available in the UK), on the web and as an app on the iPhone.

Age of onset

The age at which hearing loss occurs is crucial for the acquisition of a spoken language.

Pre-lingual deafness

Main article: Prelingual deafness

Prelingual deafness is hearing impairment that is sustained prior to the acquisition of language, which can occur as a result of a congenital condition or through hearing loss in early infancy. Prelingual deafness impairs an individual's ability to acquire a spoken language, but children born into signing families rarely have delays in language development. Most pre-lingual hearing impairment is acquired via either disease or trauma rather than genetically inherited, so families with deaf children nearly always lack previous experience with sign language.

Post-lingual deafness

Main article: Post-lingual deafness

Post-lingual deafness is hearing impairment that is sustained after the acquisition of language, which can occur as a result of disease, trauma, or as a side-effect of a medicine. Typically, hearing loss is gradual and often detected by family and friends of affected individuals long before the patients themselves will acknowledge the disability.^{[citation needed]} Common treatments include hearing aids and learning lip reading.

Post-lingual deafness is far more common than pre-lingual deafness.

Unilateral and bilateral hearing impairment

People with unilateral hearing impairment (single sided deafness/SSD) have an impairment in only one ear. This can impair a person's ability to localize sounds (e.g., determining where traffic is coming from) and distinguish sounds from background noise in noisy environments.

A similar effect can result from King-Kopetzky syndrome (also known as Auditory disability with normal hearing and obscure auditory dysfunction), which is characterized by an inability to process out background noise in noisy environments despite normal performance on traditional hearing tests. See also: "cocktail party effect", House Ear Institute's Hearing In Noise Test.

Causes

The following are some of the major causes of hearing loss.

Age

Presbycusis, the progressive loss of ability to hear high frequencies with increasing age, begins in early adulthood, but does not usually interfere with ability to understand conversation until much later. Although genetically variable it is a normal concomitant of aging and is distinct from hearing losses caused by noise exposure, toxins or disease agents.^[2]

Long-term exposure to environmental noise

Main article: Noise-induced hearing loss

Populations of people living near airports or freeways are exposed to levels of noise typically in the 65 to 75 dB(A) range. If lifestyles include significant outdoor or open window conditions, these exposures over time can degrade hearing. The U.S. EPA and various states have set noise standards to protect people from these adverse health risks. The EPA has identified the level of 70 dB(A) for 24 hour exposure as the level necessary to protect the public from hearing loss and other disruptive effects from noise, such as sleep disturbance, stress-related problems, learning detriment, etc. (EPA, 1974).

Noise-induced hearing loss (NIHL) typically is centered at 3000, 4000, or 6000 Hz. As noise damage progresses, damage starts affecting lower and higher frequencies. On an audiogram, the resulting configuration has a distinctive notch, sometimes referred to as a "noise notch." As aging and other effects contribute to higher frequency loss (6–8 kHz on an audiogram), this notch may be obscured and entirely disappear.

Louder sounds cause damage in a shorter period of time. Estimation of a "safe" duration of exposure is possible using an exchange rate of 3 dB. As 3 dB represents a doubling of intensity of sound, duration of exposure must be cut in half to maintain the same energy dose. For example, the "safe" daily exposure amount at 85 dB A, known as an exposure action value, is 8 hours, while the "safe" exposure at 91 dB(A) is only 2 hours (National Institute for Occupational Safety and Health, 1998). Note that for some people, sound may be damaging at even lower levels than 85 dB A. Exposures to other ototoxins (such as pesticides, some medications including chemotherapy, solvents, etc.) can lead to greater susceptibility to noise damage, as well as causing their own damage. This is called a synergistic interaction.

People with allergies have a higher chance of increased hearing loss. Hearing loss can be caused by the sudden change in air pressure behind the eardrum in the Eustachian Tube during a sneeze. Though the amount of hearing loss seems negligible, roughly .0001% loss per sneeze dependent upon the strength and frequency of the sneeze(s), their effects are cumulative. Allergy sufferers typically have on average 1-3% more hearing loss than those without allergies, due to their above average number of sneezes.

Some American health and safety agencies (such as OSHA-Occupational Safety and Health Administration and MSHA-Mine Safety and Health Administration), use an exchange rate of 5 dB. While this exchange rate is simpler to use, it drastically underestimates the damage caused by very loud noise. For example, at 115 dB, a 3 dB exchange rate would limit exposure to about half a minute; the 5 dB exchange rate allows 15 minutes.

While OSHA, MSHA, and FRA provide guidelines to limit noise exposure on the job, there is essentially no regulation or enforcement of sound output for recreational sources and environments, such as sports arenas, musical venues, bars, etc. This lack of regulation resulted from the defunding of ONAC, the EPA's Office of Noise Abatement and Control, in the early 1980s. ONAC was established in 1972 by the Noise Control Act and charged with working to assess and reduce environmental noise. Although the Office still exists, it has not been assigned new funding.

Many people are unaware of the presence of environmental sound at damaging levels, or of the level at which sound becomes harmful. Common sources of damaging noise levels include car stereos, children's toys, transportation, crowds, lawn and maintenance equipment, power tools, gun use, and even hair dryers. Noise damage is cumulative; all sources of damage must be considered to assess risk. If one is exposed to loud sound (including music) at high levels or for extended durations (85 dB A or greater), then hearing impairment will occur. Sound levels increase with proximity; as the source is brought closer to the ear, the sound level increases.

Genetic

Hearing loss can be inherited. Both dominant genes and recessive genes exist which can cause mild to profound impairment. If a family has a dominant gene for deafness it will persist across generations because it will manifest itself in the offspring even if it is inherited from only one parent. If a family had genetic hearing impairment caused by a recessive gene it will not always be apparent as it will have to be passed onto offspring from both parents. Dominant and recessive hearing impairment can be syndromic or nonsyndromic. Recent gene mapping has identified dozens of nonsyndromic dominant (DFNA#) and recessive (DFNB#) forms of deafness.

• The first gene mapped for non-syndromic deafness, DFNA1, involves a splice site mutation in the formin related homolog diaphanous 1 (DIAPH1). A single base change in a large Costa Rican family was identified as causative in a rare form of low frequency onset progressive hearing loss with autosomal dominant inheritance exhibiting variable age of onset and complete penetrance by age 30.^[3]
• The most common type of congenital hearing impairment in developed countries is DFNB1, also known as Connexin 26 deafness or GJB2-related deafness.
• The most common dominant syndromic forms of hearing impairment include Stickler syndrome and Waardenburg syndrome.
• The most common recessive syndromic forms of hearing impairment are Pendred syndrome, Large vestibular aqueduct syndrome and Usher syndrome.
• The congenital defect microtia can cause full or partial deafness depending upon the severity of the deformity and whether or not certain parts of the inner or middle ear are affected.
• Mutations in PTPRQ Are a Cause of Autosomal-Recessive Nonsyndromic Hearing Impairment.^[4]

Disease or illness

• Measles may result in auditory nerve damage
• Meningitis may damage the auditory nerve or the cochlea
• Autoimmune disease has only recently been recognized as a potential cause for cochlear damage. Although probably rare, it is possible for autoimmune processes to target the cochlea specifically, without symptoms affecting other organs. Wegener's granulomatosis is one of the autoimmune conditions that may precipitate hearing loss.
• Mumps (Epidemic parotitis) may result in profound sensorineural hearing loss (90 dB or more), unilateral (one ear) or bilateral (both ears).
• Presbycusis is a progressive hearing impairment accompanying age, typically affecting sensitivity to higher frequencies (above about 2 kHz).
• Adenoids that do not disappear by adolescence may continue to grow and may obstruct the Eustachian tube, causing conductive hearing impairment and nasal infections that can spread to the middle ear.
• AIDS and ARC patients frequently experience auditory system anomalies.
• HIV (and subsequent opportunistic infections) may directly affect the cochlea and central auditory system.
• Chlamydia may cause hearing loss in newborns to whom the disease has been passed at birth.
• Fetal alcohol syndrome is reported to cause hearing loss in up to 64% of infants born to alcoholic mothers, from the ototoxic effect on the developing fetus plus malnutrition during pregnancy from the excess alcohol intake.
• Premature birth results in sensorineural hearing loss approximately 5% of the time.
• Syphilis is commonly transmitted from pregnant women to their fetuses, and about a third of the infected children will eventually become deaf.
• Otosclerosis is a hardening of the stapes (or stirrup) in the middle ear and causes conductive hearing loss.
• Medulloblastoma and other types of Brain Tumors can result in hearing loss, whether by the placement of the tumor around the Vestibulocochlear nerve, surgical resection, or platinum-based chemotherapy drugs such as cisplatin.
• Superior canal dehiscence, a gap in the bone cover above the inner ear, can lead to low-frequency conductive hearing loss, autophony and vertigo

Medications

Some medications cause irreversible damage to the ear, and are limited in their use for this reason. The most important group is the aminoglycosides (main member gentamicin) and platinum based chemotherapeutics such as cisplatin.

Some medications may reversibly affect hearing. This includes some diuretics, aspirin and NSAIDs, and macrolide antibiotics. Others may cause permanent hearing loss.^[5] Extremely heavy hydrocodone (Vicodin or Lorcet) abuse is known to cause hearing impairment. Commentators have speculated that radio talk show host Rush Limbaugh's hearing loss was at least in part caused by his admitted addiction to narcotic pain killers, in particular Vicodin and OxyContin.^[6]

Exposure to ototoxic chemicals

Main article: Ototoxicity

In addition to medications, hearing loss can also result from specific drugs; metals, such as lead; solvents, such as toluene (found in crude oil, gasoline^[7] and automobile exhaust,^[7] for example); and asphyxiants.^[8] Combined with noise, these ototoxic chemicals have an additive effect on a person’s hearing loss.^[8] Hearing loss due to chemicals starts in the high frequency range and is irreversible. It damages the cochlea with lesions and degrades central portions of the auditory system.^[8] For some ototoxic chemical exposures, particularly styrene,^[9] the risk of hearing loss can be higher than being exposed to noise alone. Controlling noise and using hearing protectors are insufficient for preventing hearing loss from these chemicals. However, taking antioxidants helps prevent ototoxic hearing loss, at least to a degree.^[9] The following list provides an accurate catalogue of ototoxic chemicals:^[8][9]

• Drugs
  • antimalarial, antibiotics, anti-inflammatory (non-steroidal), antineoplastic, diuretics
• Solvents
  • toluene, styrene, xylene, n-hexane, ethyl benzene, white spirits/Stoddard, carbon disulfide, fuels, perchloroethylene, trichloroethylene, p-xylene
• Asphyxiants
  • carbon monoxide, hydrogen cyanide
• Metals
  • lead, mercury, organotins (trimethyltin)
• Pesticides/Herbicides
  • paraquat, organophosphates

Physical trauma

There can be damage either to the ear itself or to the brain centers that process the aural information conveyed by the ears.

People who sustain head injury are especially vulnerable to hearing loss or tinnitus, either temporary or permanent. I. King Jordan lost his hearing after suffering a skull fracture as a result of a motorcycle accident at age 21.^[10]

Management

Approaches

If the hearing loss occurs at a young age, interference with the acquisition of spoken language and social skills may occur.^{[original research?]} Hearing aids, which amplify the incoming sound, may alleviate some of the problems caused by hearing impairment, but are often insufficient. Cochlear implants artificially stimulate the VIIIth Nerve by providing an electric impulse substitution for the firing of hair cells. Cochlear implants are not only expensive, but require sophisticated programming in conjunction with patient training for effectiveness. The United States Food and Drug Administration reported that cochlear implant recipients may be at higher risk for meningitis.^[11] People who have hearing impairments, especially those who develop a hearing problem in childhood or old age, may need the support and technical adaptations as part of the rehabilitation process. Recent research shows variations in efficacy but some studies ^[12] show that if implanted at a very young age, some profoundly impaired children can acquire effective hearing and speech, particularly if supported by appropriate rehabilitation such as auditory-verbal therapy.^[13]

Views of treatments

There has been considerable controversy within the culturally Deaf community over cochlear implants. For the most part, there is little objection to those who lost their hearing later in life or culturally Deaf adults (voluntarily) choosing to be fitted with a cochlear implant.

Many in the Deaf community strongly object to a deaf child being fitted with a cochlear implant (often on the advice of an audiologist; new parents may not have sufficient information on raising deaf children and placed in an oral-only program that emphasizes the ability to speak and listen over other forms of communication such as sign language or total communication. This may be because not all audiologists are familiar with the benefits of sign language to the deaf child and family. Other concerns include loss of deaf culture and limitations on hearing restoration.

Most parents and doctors tell children not to play sports or get involved in activities that can result in injuries to the head. Soccer, Hockey, and Basketball can be some examples. A child with a hearing loss may prefer to stay away from noisy places, such as rock concerts, Football games, airports, etc., as this can cause noise overflow (noise overflow is a type of headache that occurs in many children and adults when they are near loud noises.)

Gene therapy

A 2005 study achieved successful regrowth of cochlea cells in guinea pigs.^[14] It is important to note, however, that the regrowth of cochlear hair cells does not imply the restoration of hearing sensitivity as the sensory cells may or may not make connections with neurons that carry the signals from hair cells to the brain. A 2008 study has shown that gene therapy targeting Atoh1 can cause hair cell growth and attract neuronal processes in embryonic mice. It is hoped that a similar treatment will one day ameliorate hearing loss in humans.^[15]

Assistive techniques and devices for hearing impairment

Many hearing impaired individuals use assistive devices in their daily lives:

• Individuals can communicate by telephone using telecommunications device for the deaf (TDD). These devices look like typewriters or word processors and transmit typed text over regular telephone lines. Other names in common use are textphone and minicom.
• There are several new Telecommunications Relay Service technologies including IP Relay and captioned telephone technologies. In the U.S., the UK, the Netherlands and many other western countries, there are Telecommunications Relay Services so that a hearing-impaired person can communicate over the phone with a hearing person via a human translator. Wireless, Internet and mobile phone/SMS text messaging are beginning to take over the role of the TDD.
• Real-time text technologies, involving streaming text that is continuously transmitted as it is typed or otherwise composed. This allows conversational use of text. Software programs are now available that automatically generate a closed-captioning of conversations. Examples include discussions in conference rooms, classroom lectures, and/or religious services. One such example of an available product is Auditory Sciences' Interact-AS product suite.^[16]
• Instant messaging software. In addition, AOL Instant Messenger provides a real-time text feature called Real-Time IM.^[17][18]
• Videophones and similar video technologies can be used for distance communication using sign language. Video conferencing technologies permit signed conversations as well as permitting a sign language–English interpreter to voice and sign conversations between a hearing impaired person and that person's hearing party, negating the use of a TTY device or computer keyboard.
• Video Relay Service and Video Remote Interpreting (VRI) services also use a third-party telecommunication service to allow a deaf or hard-of-hearing person to communicate quickly and conveniently with a hearing person, through a sign language interpreter.
• Phone captioning is a service in which a hearing person's speech is captioned by a third party, enabling a hearing impaired person to conduct a conversation with a hearing person over the phone.^[19]
• For mobile phones, software apps are available to provide TDD/textphone functionality on some carriers/models to provide 2-way communications.
• Hearing dogs are a specific type of assistance dog specifically selected and trained to assist the deaf and hearing impaired by alerting their handler to important sounds, such as doorbells, smoke alarms, ringing telephones, or alarm clocks.
• Other assistive devices include those that use flashing lights to signal events such as a ringing telephone, a doorbell, or a fire alarm.
• The advent of the Internet's World Wide Web and closed captioning has given the hearing impaired unprecedented access to information. Electronic mail and online chat have reduced the need for deaf and hard-of-hearing people to use a third-party Telecommunications Relay Service in order to communicate with the hearing and other hearing impaired people;

Further information: List of video telecommunication services and product brands, Video Relay Service, and Video Remote Interpreting

Resources and interventions

Many different assistive technologies, such as hearing aids, are available to those who are hearing impaired. People with cochlear implants, hearing aids, or neither of these devices can also use additional communication devices to reduce the interference of background sounds, or to mediate the problems of distance from sound and poor sound quality caused by reverberation and poor acoustic materials of walls, floors and hard furniture.

Three types of wireless devices exist along with hard-wired devices. A wireless device used by people who use their residual hearing has two main components. One component sends the sound out to the listener, but is not directly connected to the listener with the hearing loss. The second component of the wireless system, the receiver, detects the sound and sends the sound to the ear of the person with the hearing loss. The three types of wireless devices are the FM system, the audio induction loop and the infra red system. Each system has advantages and benefits for particular uses.

The FM system can easily operate in many environments with battery power. It is thus mobile and does not usually require a sound expert for it to work properly. The listener with the hearing loss carries a receiver and an earpiece. Another wireless system is the audio induction loop which permits the listener with hearing loss to be free of wearing a receiver provided that the listener has a hearing aid or cochlear implant processor with an accessory called a "telecoil". If the listener does not have a telecoil, then he or she must carry a receiver with an earpiece.

A third kind of wireless device for people with hearing loss is the infra red (IR) system, which also requires a receiver to be worn by the listener. Usually the emitter for the IR device, that is, the component that sends out the signal, uses an AC adaptor. The advantage of the IR wireless system is that people in adjoining rooms cannot listen in on conversations, making it useful for situations where privacy and confidentiality are required. Another way to achieve confidentiality is to use a hardwired amplifier which sends out no signal beyond the earpiece that is plugged directly into the amplifier. That amplifier of the hardwired device also has a microphone inside of it or plugged into it.

Inside the classroom, children with hearing impairments may also benefit from interventions. These include providing favorable seating for the child. This can be achieved by having the student sit as close to the teacher as possible so that they will be able to hear the teacher, or read their lips more easily. When lecturing, teachers should try to look at the student as much as possible and limit unnecessary noise in the classroom. If a student has a hearing aid, they are likely to hear a lot of unwanted noises.

Pairing hearing impaired students with hearing students is a common technique, allowing the non-hearing student to ask the hearing student questions about concepts that they have not understood. When teaching students with hearing impairments, overheads are commonly used, allowing the teacher to write, as well as maintain visual focus on the hearing impaired student. For those students who are completely deaf, one of the most common interventions is having the child communicate with others through an interpreter using sign language.^[20]

Epidemiology

Disability-adjusted life year for hearing loss (adult onset) per 100,000 inhabitants in 2002.^[21]

  no data

  less than 150

  150–200

  200–250

  250–300

  300–350

  350–400

  400–450

  450–500

  500–550

  550–600

  600–650

  more than 650

Hearing loss in children

12% of children aged 6–19 years have permanent hearing damage from excessive noise exposure.^[22] The American Academy of Pediatrics advises that children should have their hearing tested several times throughout their schooling:^[22]

• When they enter school
• At ages 6, 8, and 10,
• At least once during middle school
• At least once during high school

Besides screening children for hearing loss, schools can also educate them on the perils of hazardous noise exposure. Research has shown that people who are educated about noise-induced hearing loss and prevention are more likely to use hearing protectors at work or in their private lives.^[22]

Myths regarding people with hearing losses

There are many myths regarding people with hearing losses including, but not limited to:

1. Everyone who is deaf or hard of hearing uses sign language.
   • There are a variety of different sign systems used by hearing-impaired individuals.^[23]
   • Individuals who experience hearing loss later in life usually do not know sign language.^[24]
   • People who are educated in the method of oralism or mainstream do not always know sign language.
2. People who cannot hear are not allowed to drive.
   • Deaf people may use special devices to alert them to sirens or other noises, or panoramic mirrors to enable improved visibility.^[25]
   • Many countries allow deaf people to drive, although at least 26 countries do not allow deaf citizens to hold a driver's license.^[25]
3. All forms of hearing loss can be solved by hearing aids or Cochlear Implants.
   • While many hearing-impaired individuals do use hearing aids, others may not benefit from the use of a hearing aid.^[23]
   • For some hearing-impaired individuals who experience distortion of incoming sounds, a Cochlear Implant may actually worsen the distortion.^[23]
4. A lack of hearing correlates to a lack of intelligence.
   • A person's intelligence level is unrelated to whether or not the person can hear.^{[citation needed]}
5. All deaf/hard of hearing people are experts in Deaf Culture.
   • Deaf people may have a variety of different beliefs, experiences, and methods of communication.^[24]
   • This may be influenced by the age at which hearing was lost and the individual's personal background.^[24]
6. All deaf people want to be hearing.
   • While some individuals with hearing loss want to become hearing, this is not the case for everyone. Some take pride in their deafness or view themselves as a minority rather than a disability group.^[26]
7. People who can't hear can't use a phone.
   • Teletypewriters, Video phones and cell phone text messages are used by deaf people to communicate. A hearing person may use an ordinary telephone and a Telecommunications Relay Service to communicate with a deaf person.
8. Everyone who cannot hear can lip read.
   • Only about 30% of spoken English is visible on the lips.^{[23][24][unreliable source?]}
   • Lip reading requires not only good lighting, but also a good understanding of the spoken language in question and may also depend on contextual knowledge about what is being said.^[24]
9. Most deaf people have deaf parents.
   • Less than 5% of deaf children in the United States have a deaf parent.^[27]

Social consequences

Pre-lingual hearing loss

See also: Prelingual deafness

In children, hearing loss can lead to social isolation for several reasons. First, the child experiences delayed social development that is in large part tied to delayed language acquisition. It is also directly tied to their inability to pick up auditory social cues. This can result in a deaf person becoming generally irritable. A child who uses sign language, or identifies with the Deaf sub-culture does not generally experience this isolation, particularly if he/she attends a school for the deaf, but may conversely experience isolation from his parents if they do not know sign language.^{[citation needed]} A child who is exclusively or predominantly oral (using speech for communication) can experience social isolation from his or her hearing peers, particularly if no one takes the time to explicitly teach her social skills that other children acquire independently by virtue of having normal hearing.^{[citation needed]} Finally, a child who has a severe impairment and uses some sign language may be rejected by Deaf peers, because of an understandable hesitation in abandoning the use of existent verbal and speech-reading skills. Some in the Deaf community can view this as a rejection of their own culture and its mores, and therefore will reject the individual preemptively.^{[citation needed]}

Post-lingual hearing loss

See also: Post-lingual deafness

Those who lose their hearing later in life, such as in late adolescence or adulthood, face their own challenges, living with the adaptations that make it possible for them to live independently. They may have to adapt to using hearing aids or a cochlear implant, develop speech-reading skills, and/or learn sign language. The affected person may need to use a TTY (teletypewriter), interpreter, or relay service to communicate over the telephone. Loneliness and depression can arise as a result of isolation (from the inability to communicate with friends and loved ones) and difficulty in accepting their disability. The challenge is made greater by the need for those around them to adapt to the person's hearing loss.

Many relationships can suffer because of emotional conflicts that occur when there are general miscommunications between family members. Generally, it's not only the person with a hearing disability that feels isolated, but others around them who feel they are not being "heard" or paid attention to, especially when the hearing loss has been gradual. Family members then feel as if their hearing loss partner doesn't care about them enough to make changes to reduce their disability and make it easier to communicate.

Within school settings

Government policies

Those who are hearing disabled do have access to a free and appropriate public education. If a child does qualify as being hearing impaired and receives an individualized education plan, the IEP team must consider, “the child’s language and communication needs. The IEP must include opportunities for direct communication with peers and professionals. It must also include the student’s academic level, and finally must include the students full range of needs”^[28] The government also distinguishes between deafness from hearing loss. The U.S. Department of Education states that deafness is hearing that is so severe that a person cannot process any type of oral information even if that person has some sort of hearing-enhancing device. The U.S. Department of Education states that a hearing impairment is when a person’s education is affected by how much that person is able to hear. This definition is not included under the term deafness. In order for a person to qualify for special services, the person’s has to hear more than 20 decibels and their educational performance must be affected by their hearing loss. This is what the government has to say about governmental policies and individualized services.

Inclusion vs. pullout

Because a hearing impairment is a disability that is prevalent in many children throughout the United States today, one may be asking themselves what is the best schooling environment for these students. There have been many mixed opinions on the subject between those who live in Deaf communities, and those who have deaf family members who do not live in Deaf communities. Deaf communities are those communities where only sign languages are typically used.

Many parents who have a child with a hearing impairment prefer their child to be in the least restrictive environment of their school. This may be because most children with hearing loss are born to hearing parents. This can also be because of the recent push for inclusion in the public schools.

It is commonly misunderstood that least restrictive environment means mainstreaming or inclusion. Sometimes the resources available at the public schools do not match up to the resources at a residential school for the deaf. Many hearing parents choose to have their deaf child educated in the general education classroom as much as possible because they are told that mainstreaming is the least restrictive environment, which is not always the case. However, there are those parents, some of which who live in Deaf communities feel that the general education classroom is not the least restrictive environment for their child. These parents feel that placing their child in a residential school where all children are deaf may be more appropriate for their child because the staff tend to be more aware of the needs and struggles of deaf children. Another reason that these parents feel a residential school may be more appropriate is because in a general education classroom, the student will not be able to communicate with their classmates due to the language barrier.

In a residential school where all the children use the same language (whether it be a school using ASL, Total Communication or Oralism), students will be able to interact normally with other students, without having to worry about being criticized. An argument supporting inclusion, on the other hand, exposes the student to people who aren't just like them, preparing them for adult life. Through interacting, children with hearing disabilities can expose themselves to other cultures which in the future may be beneficial for them when it comes to finding jobs and living on their own in a society where their disability may put them in the minority. These are some reasons why a person may or may not want to put their child in an inclusion classroom.^[28]

See also

Disability portal

• Audism - discrimination against the deaf and hearing impaired
• Deafblind
• Deafhood
• Deaf culture
• National Association for the Deaf (NAD)
• Auditory brainstem response (ABR) test
• Auditory Neuropathy Spectrum Disorder (ANSD)
• Auditory Processing Disorder
• Spatial hearing loss
• Closed captioning
• Teleprinter (TTY)
• Hearing loss with craniofacial syndromes
• IFHOHYP - International Federation of Hard of Hearing Young People
• Kay's Tutor v Ayrshire & Arran Health Board
• King-Kopetzky syndrome
• Models of deafness (a comparison of the medical, disability and cultural models of deafness)
• Mondini dysplasia
• NIOSH Power Tools Database
• Noise induced hearing loss
• Noise pollution
• Occupational health and safety awards
• Post-lingual deafness
• Pre-lingual deafness
• Royal National Institute for Deaf People
• Deaf animals
• Safe-In-Sound Award
• Tinnitus
• Unilateral hearing loss
• Videophone
• Youth hearing conservation programs
• Gallaudet University
• National Technical Institute for the Deaf (NTID)

References

1. ^ eBook: Current Diagnosis & Treatment in Otolaryngology: Head & Neck Surgery, Lalwani, Anil K. (Ed.) Chapter 44: Audiologic Testing by Robert W. Sweetow, PhD, Jennifer McKee Bold, AuD, Access Medicine
2. ^ Robinson, DW; Sutton, GJ (1979). "Age effect in hearing - a comparative analysis of published threshold data". Audiology : official organ of the International Society of Audiology 18 (4): 320–34. PMID 475664. 
3. ^ Lynch, ED; Lee, MK; Morrow, JE; Welcsh, PL; Le�n, PE; King, MC (1997). "Nonsyndromic deafness DFNA1 associated with mutation of a human homolog of the Drosophila gene diaphanous". Science 278 (5341): 1315–8. doi:10.1126/science.278.5341.1315. PMID 9360932. 
4. ^ Schraders M, Oostrik J, Huygen PL, Strom TM, van Wijk E, Kunst HP, Hoefsloot LH, Cremers CW, Admiraal RJ, Kremer H (Mar 2010). "Mutations in PTPRQ Are a Cause of Autosomal-Recessive Nonsyndromic Hearing Impairment DFNB84 and Associated with Vestibular Dysfunction". The American Journal of Human Genetics 86 (4): 604–10. doi:10.1016/j.ajhg.2010.02.015. PMC 2850434. PMID 20346435. http://www.pubmedcentral.nih.gov/articlerender.fcgi?tool=pmcentrez&artid=2850434. 
5. ^ http://www.asha.org/public/hearing/Ototoxic-Medications/
6. ^ Tim Grieve (October 7, 2003). "Did popping painkillers make Rush lose his hearing?". Salon.com. http://dir.salon.com/story/news/feature/2003/10/07/rush_drugs/index.html. Retrieved 2008-09-08. 
7. ^ ^{a b} "Tox Town – Toluene – Toxic chemicals and environmental health risks where you live and work – Text Version". toxtown.nlm.nih.gov. http://toxtown.nlm.nih.gov/text_version/chemicals.php?id=30. Retrieved 2010-06-09. 
8. ^ ^{a b c d} Thais C. Morata. "Addressing the Risk for Hearing Loss from Industrial Chemicals". cdc.gov. http://www.cdc.gov/niosh/topics/noise/pubs/presentations/AOHC.swf. Retrieved 2008-06-05. 
9. ^ ^{a b c} Johnson, Ann-Christin. "Occupational exposure to chemicals and hearing impairment – the need for a noise notation" (PDF). Karolinska Institutet: 1–48. http://awww.arbetsmiljoverket.se/dokument/arkiv/neg/Chemicals_and_hearing_impairment.pdf. Retrieved 2009-06-19. 
10. ^ "The World of the Deaf," The Washington Post, February 26, 1978, p. G1.
11. ^ "FDA Public Health Notification: Risk of Bacterial Meningitis in Children with Cochlear Implants". FDA. July 24, 2002. http://www.fda.gov/cdrh/safety/cochlear.html. Retrieved 2008-11-09. 
12. ^ Elliot & Oliver'S Story – Research
13. ^ Research articles supporting auditory verbal therapy
14. ^ Andy Coghlan (2005-02-14). "Gene therapy is first deafness 'cure'". NewScientist.com News Service. http://www.newscientist.com/article.ns?id=dn7003. 
15. ^ Gubbels, SP; Woessner, DW; Mitchell, JC; Ricci, AJ; Brigande, JV (2008). "Functional auditory hair cells produced in the mammalian cochlea by in utero gene transfer". Nature 455 (7212): 537–41. doi:10.1038/nature07265. PMC 2925035. PMID 18754012. http://www.pubmedcentral.nih.gov/articlerender.fcgi?tool=pmcentrez&artid=2925035. 
16. ^ http://www.auditorysciences.com Auditory Sciences website
17. ^ http://tap.gallaudet.edu/Text/AOL/default.asp
18. ^ http://help.aol.com/help/microsites/microsite.do?cmd=displayKC&docType=kc&externalId=223568
19. ^ Free Phone Caption Service for the Deaf, Hard of Hearing, and hearing impared [sic]. PhoneCaption.com. Retrieved on 2010-12-10.
20. ^ An Educators Guide to Hearing Disability Issues. (n.d.). Retrieved July 19, 2009 & Facts About Hearing Loss. (2005). Retrieved July 19, 2009, from Alexander Bell Association for the Deaf and Hard of Hearing
21. ^ "Mortality and Burden of Disease Estimates for WHO Member States in 2002" (xls). World Health Organization. 2002. http://www.who.int/entity/healthinfo/statistics/bodgbddeathdalyestimates.xls. 
22. ^ ^{a b c} "Noise-Induced Hearing Loss: Promoting Hearing Health Among Youth" CDC Healthy Youth!: 1-7-09
23. ^ ^{a b c d} Myths About Deaf and Hard of Hearing. Tutorworkshop.org. Retrieved on 2010-12-10.
24. ^ ^{a b c d e} What Do You Know About Deaf Culture?
25. ^ ^{a b} Sound and Fury – Deaf Culture – Living with Deafness. Pbs.org. Retrieved on 2010-12-10.
26. ^ http://ifmyhandscouldspeak.wordpress.com/common-myths-about-deaf-people-and-the-truth/
27. ^ Mitchell Ross E., Karchmer Michael A. (2004). "Chasing the mythical ten percent: Parental hearing status of deaf and hard of hearing students in the United States". Sign Language Studies 4 (2): 138–163. doi:10.1353/sls.2004.0005. 
28. ^ ^{a b} Smith, D. D., & Tyler, N. C. (2010). Introduction to Special Education. Columbus: Merrill.

Bibliography

• United States Environmental Protection Agency press release, April 2, 1974

External links

• Specialist Library for ENT and Audiology High quality research and patient information on audiology and hearing impairment
• American Hearing Research Foundation Northwestern University's partner in leading hearing research in the United States.
• A frequency sweep to determine the listener's high frequency hearing limit
• GeneReviews/NCBI/NIH/UW entry on Deafness and Hereditary Hearing Loss Overview
• Australian Federation of Deaf Societies – Also called AFDS, the peak body for Deaf services in Australia.
• http://www.direct.gov.uk/disability Directgov disabled people – UK Govt information
• Deafness Research UK - Medical research charity focusing on hearing loss, deafness and related conditions
• World Health Organization fact sheet on deafness and hearing impairment
• National Association of the Deaf. The NAD protects deaf and hard of hearing civil rights.
• International Federation of Hard Of Hearing Young People
• Hearing Loss Association of America Nations Voice for People with Hearing Loss
• Stop CMV – The CMV Action Network Congenital CMV is a leading cause of hearing impariment.
• NIOSH Power Tools Database The database gives information about sound power levels and sound pressure levels for various power tools.
• NIOSH Hearing Loss Prevention Strategic Goals
• A New Reason for Why the Deaf May Have Trouble Reading, an April 2011 radio and Internet report by the Special English service of the Voice of America.
• Simulations of hearing loss, including loudness recruitment and spectral smearing