- Tracheobronchomegaly
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Mounier-Kuhn syndrome Classification and external resources ICD-9 748.3 OMIM 275300 DiseasesDB 31501 MeSH D014137 Mounier-Kuhn syndrome (also called tracheobronchomegaly) is a very rare[1] disease of the lungs and airways where the trachea and bronchi become abnormally wide.[2] This leads to sputum collection in the lungs which results in repeated chest infections and bronchiectasis.[1]
History
The term "Mounier-Kuhn syndrome" derives from the characterization of the condition by Mounier-Kuhn in 1932, while the name "tracheobronchomegaly" was introduced by Katz et al. in 1962.[3][4][5]
References
- ^ a b Menon B, Aggarwal B, Iqbal A (2008). "Mounier-Kuhn syndrome: report of 8 cases of tracheobronchomegaly with associated complications". South Med J. 101 (1): 83–87. doi:10.1097/SMJ.0b013e31815d4259. PMID 18176298.
- ^ Schwartz, W; Rossoff L (Nov 1994). "Tracheobronchomegaly" (PDF). Chest (American College of Chest Physicians) 106 (5): 1589–1590. doi:10.1378/chest.106.5.1589. PMID 7956426. http://www.chestjournal.org/cgi/reprint/106/5/1589. Retrieved 2008-02-27.
- ^ PMID 8091335
- ^ PMID 13958486
- ^ Mounier-Kuhn P. Dilatation de la trachée: constatations radiographiques etbronchoscopiques. Lyon Med. 1932;150:106-9.
Congenital malformations and deformations of respiratory system (Q30–Q34, 748) Upper RT Lower RT Trachea and bronchusBronchiectasis · Pulmonary hypoplasia · Pulmonary sequestration · Congenital cystic adenomatoid malformationCategories:- Congenital disorders of respiratory system
- Rare diseases
- Syndromes
- Disease stubs
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