Name = PAGENAME
DiseasesDB = 29496
ICD10 = ICD10|D|30|0|d|10
ICD9 = ICD9|223.0
ICDO = M8860/0
MeshID = D018207
Angiomyolipoma is a benign renal neoplasm previously considered to be a
hamartomaor choristoma, but now known to be neoplastic. [Eble JN. Angiomyolipoma of the kidney. Semin Diagn Pathol 1988;15:21-40] It is composed of variable amounts of fat, vascular, and smooth muscleelements. The fat density of the tumour on CThas been regarded to be pathognomonic, although there are now case reports of renal cell carcinoma types also possessing macroscopic fat.
The lesion is well demarcated and contains mature elements. It occurs in more than 50% of individuals with
tuberous sclerosis, often bilaterally. Angiomyolipomata also occur in 40% of women who have a rare, cystic lung disease called lymphangioleiomyomatosis, or LAM.cite journal |author=McCormack FX |title=Lymphangioleiomyomatosis |journal=MedGenMed |volume=8 |issue=1 |pages=15 |year=2006 |pmid=16915145 |pmc=1682009 |doi= |url=http://www.medscape.com/viewarticle/518317]
* [http://www.thelamfoundation.org/ The LAM Foundation (US)]
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