- Angiomyolipoma
Infobox_Disease
Name = PAGENAME
Caption =
DiseasesDB = 29496
ICD10 = ICD10|D|30|0|d|10
ICD9 = ICD9|223.0
ICDO = M8860/0
OMIM =
MedlinePlus =
eMedicineSubj =
eMedicineTopic =
MeshID = D018207Angiomyolipoma is a benign renal neoplasm previously considered to be a
hamartoma orchoristoma , but now known to beneoplastic . [Eble JN. Angiomyolipoma of the kidney. Semin Diagn Pathol 1988;15:21-40] It is composed of variable amounts offat , vascular, andsmooth muscle elements. The fat density of the tumour onCT has been regarded to bepathognomonic , although there are now case reports of renal cell carcinoma types also possessing macroscopic fat.The lesion is well demarcated and contains mature elements. It occurs in more than 50% of individuals with
tuberous sclerosis , often bilaterally. Angiomyolipomata also occur in 40% of women who have a rare, cystic lung disease called lymphangioleiomyomatosis, or LAM.cite journal |author=McCormack FX |title=Lymphangioleiomyomatosis |journal=MedGenMed |volume=8 |issue=1 |pages=15 |year=2006 |pmid=16915145 |pmc=1682009 |doi= |url=http://www.medscape.com/viewarticle/518317]ee also
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PEComa
=AdditionalReferences
External links
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* [http://www.thelamfoundation.org/ The LAM Foundation (US)]
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