Cruveilhier–Baumgarten disease
- Cruveilhier–Baumgarten disease
-
Cruveilhier-Baumgarten disease or Pégot-Cruveilhier-Baumgarten disease is a rare medical condition in which the umbilical or paraumbilical veins are distended, with an abdominal wall bruit (the Cruveilhier-Baumgarten bruit) and palpable thrill, portal hypertension with splenomegaly, hypersplenism and oesophageal varices, with a normal or small liver.
It was first described by Pégot in 1833, and then by Jean Cruveilhier (1835) and Paul Clemens von Baumgarten (1907).[1]
Armstrong et al. (1942) and Steinburg and Galambos (1967) described two different types of the condition:
- Cruveilhier-Baumgarten syndrome: liver cirrhosis or portal hypertension is the cause of the distension of the paraumbilical veins (i.e. an acquired condition in which the veins reopen due to high portal pressure).
- Cruveilhier-Baumgarten disease: the distension of the paraumbilical veins is due to failure of umbilical vein closure, with little or no evidence of liver disease found on liver biopsy (i.e. a congenital patency of the umbilical vein leading to portal hypertension).[1]
External links
Cruveilhier-Baumgarten disease at Who Named It?
References
Wikimedia Foundation.
2010.
Look at other dictionaries:
Cruveilhier–Baumgarten bruit — The Cruveilhier Baumgarten bruit is a clinical sign which can be found in Cruveilhier Baumgarten disease. In this condition there are prominent umbilical and paraumbilical veins; auscultation over these vessels may reveal a humming sound (i.e. a… … Wikipedia
Disease — Illness or sickness often characterized by typical patient problems (symptoms) and physical findings (signs). Disruption sequence: The events that occur when a fetus that is developing normally is subjected to a destructive agent such as the… … Medical dictionary
Baumgarten — Paul Clemens von, German pathologist, 1848–1928. See B. veins, under vein, Cruveilhier B. disease, Cruveilhier B. murmur, Cruveilhier B. sign, Cruveilhier B. syndrome … Medical dictionary
Cruveilhier — Jean, French pathologist and anatomist, 1791–1874. See C. fascia, C. fossa, fossa navicularis C., C. joint, C. ligaments, under ligament, C. plexus, C. Baumgarten disease, C. Baumgarten murmur, C. Baumgarten sign, C. Baumgarten syndrome … Medical dictionary
Jean Cruveilhier — (born 1791 in Limoges, France; died 1874 in Sussac) was a French anatomist.He was educated at the University of Paris, where in 1825 he succeeded Pierre Augustin Béclard (1785 1825) as professor of anatomy. In 1836 he relinquished the chair of… … Wikipedia
Paul Clemens von Baumgarten — (born August 28, 1848, Dresden; died 1928, Tübingen) was a German pathologist. He was the son of a physician, and was a pupil of Christian Wilhelm Braune (1831 1892) and Ernst Leberecht Wagner (1829 1888) in Leipzig, and Ernst Neumann (1834 1918) … Wikipedia
List of eponymous diseases — An eponymous disease is one that has been named after the person who first described the condition. This usually involves publishing an article in a respected medical journal. Rarely an eponymous disease may be named after a patient (examples… … Wikipedia
syndrome — The aggregate of symptoms and signs associated with any morbid process, and constituting together the picture of the disease. SEE ALSO: disease. [G. s., a running together, tumultuous concourse; (in med.) a concurrence of symptoms, fr. syn,… … Medical dictionary
Liste der Syndrome — Diese Seite listet in alphabetischer Reihenfolge und ohne Anspruch auf Vollständigkeit Syndrome und Komplexe aus unterschiedlichen medizinischen Fachgebieten auf. Bitte nur Verweise auf den tatsächlichen Titel des Beitrags und keine… … Deutsch Wikipedia
Murmur — A Murmur is an abnormal "whooshing" sound created by blood flow through heart valves, as well as flow through chamber narrowings or unusual connections seen with congenital heart disease. It is usually heard by the doctor while… … Medical dictionary
