- Pulmonary valve stenosis
Name = PAGENAME
Caption = Pulmonary valve stenosis
Width = 250px
DiseasesDB = 11025
ICD10 = ICD10|I|37|0|i|30, ICD10|I|37|2|i|30, ICD10|Q|22|1|q|20
ICD9 = ICD9|424.3, ICD9|746.02
OMIM = 265500
MedlinePlus = 001096
eMedicineSubj = emerg
eMedicineTopic = 491
MeshID = D011666
Pulmonary valve stenosis is a
valvular heart diseasein which outflow of blood from the right ventricleof the heartis obstructed at the level of the pulmonic valve. This results in the reduction of flow of bloodto the lungs. Valvular pulmonic stenosis accounts for 80% of right ventricular outflow tract obstruction.cite book | coauthors=Edmund Kenneth Kerut, Elizabeth F. McIlwain, Gary D. Plotnick | title=Handbook of Echo-Doppler Interpretation | publisher=Futura | date=1996 | location=Armonk, NY, U.S.A. | pages=115-6 | id=ISBN 0-87993-636-3] While the most common cause of pulmonary valve stenosis is congenital heart disease, it may also be due to rheumatic heart disease or a malignant carcinoidtumor.
jugular venous distention, cyanosis(usually visible in the nailbeds), right ventricular hypertrophyand general symptoms of lowered oxygenation of the blood. When the stenosis is mild, it can go unnoticed for many years. If stenosis is severe, you may see sudden fainting or dizziness if exercised too much, you may also experience an enlarged liver (hepatomegaly) and swelling in the legs (edema).
The initial evaluation of pulmonary valve stenosis involves echocardiography. The degree of stenosis is typically determined by the peak pressure gradient across the valve. If the peak gradient across the valve is greater than 50 mmHg, intervention is generally warranted. If the peak gradient is < 25 mmHg, no intervention is generally needed. If the gradient is between 25 and 50 mmHg, it is a gray area.
Valve replacement or surgical repair (depending upon whether the stenosis is in the valve or vessel) may be indicated. If the valve stenosis is of congenital origin, balloon valvuloplasty is another option.
* [http://www.umm.edu/ency/article/001096.htm Overview] at University of Maryland
* [http://www.americanheart.org/presenter.jhtml?identifier=11070 Overview] at
American Heart Association
* [http://heartcenter.seattlechildrens.org/conditions_treated/pulmonary_stenosis.asp Pulmonary Stenosis information] from Seattle Children's Hospital Heart Center
* [http://www.aboutkidshealth.ca/HeartConditions/Pulmonary-Stenosis.aspx?articleID=6703&categoryID=HC-nh2-04o Animation of pulmonary stenosis] from AboutKidsHealth.ca
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