Name = PAGENAME
ICD10 = ICD10|M|72|9|m|70
MeshID = D005350
The term fibromatosis refers to a group of
benign soft tissue tumors ( fibromas) [DorlandsDict|three/000040062|fibromatosis] which have certain characteristics in common, including absence of cytologic and clinical malignantfeatures, a histologyconsistent with proliferation of well-differentiated fibroblasts, an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence.
Other names include "musculoaponeurotic fibromatosis," referring to the tendency of these tumors to be adjacent to and infiltrating deep
skeletal muscle, and "desmoid tumor," an obsolete term which more specifically refers to the occurrence of these tumors in the abdominal wallof a pregnant woman.
Fibromatosis is a different entity from
Treatment includes prompt radical excision with a wide margin and/or radiation. Despite the local infiltrative and aggressive behavior of these tumors, mortality secondary to these tumors is minimal to nonexistent.
Subtypes of fibromatosis include -
*infantile digital fibromatosis
*fibromatosis hyalinica multiplex
*penile fibromatosis (
*palmar fibromatosis (
Multiple fibromatoses are seen in
Gardner's syndrome, a syndrome which also includes multiple colon polyps and osteomas.
* [http://www.maxillofacialcenter.com/BondBook/softtissue/fibromatosis.html maxillofacialcenter]
* Rosai, J. "Rosai and Ackerman's Surgical Pathology". Mosby Inc., 2004. pg 2249-2252.
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