Histidine ammonia-lyase

Histidine ammonia-lyase

Name=histidine ammonia-lyase


Histidine ammonia-lyase (or histidase) is an enzyme which converts histidine into ammonia and urocanic acid.


Mutations in the gene for histidase are associated with histidinemia and urocanic aciduria.

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  • histidine ammonia-lyase — his·ti·dine am·mo·nia ly·ase (hisґtĭ dēn ə moґne ə liґās) [EC] an enzyme of the lyase class that catalyzes the deamination of histidine to urocanate, the initial step of histidine catabolism. Deficiency of the… …   Medical dictionary

  • ammonia-lyase — am·mo·nia ly·ase (ə mōnґyə liґās) [EC 4.3.1] a sub subclass of enzymes of the lyase class that catalyze the formation of a C C bond in a molecule by liberation of ammonia, e.g., histidine ammonia lyase …   Medical dictionary

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  • Amino acid — This article is about the class of chemicals. For the structures and properties of the standard proteinogenic amino acids, see Proteinogenic amino acid. The generic structure of an alpha amino acid in its unionized form …   Wikipedia

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