Carnitine O-palmitoyltransferase

Carnitine O-palmitoyltransferase

Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase or carnitine acyltransferase) is a mitochondrial transferase enzyme (EC number|2.3.1.21) involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA.

Molecules

Pathway

Human forms of CPT

There are four different forms of CPT in humans:

* CPT1A - associated with Carnitine palmitoyltransferase I deficiency
* CPT1B
* CPT1C
* CPT2 - associated with Carnitine palmitoyltransferase II deficiency

ee also

* Fatty_acid_degradation#Transport_into_the_mitochondrial_matrix

External links

* - Acyltransferases ChoActase / COT / CPT family in PROSITE
* [http://pfam.sanger.ac.uk/family?entry=PF00755 Choline/Carnitine o-acyltransferase family] in Pfam
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Look at other dictionaries:

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  • Carnitine palmitoyltransferase II deficiency — Classification and external resources Carnitine ICD 9 …   Wikipedia

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  • Carnitine O-octanoyltransferase — In enzymology, a carnitine O octanoyltransferase (EC number|2.3.1.137) is an enzyme that catalyzes the chemical reaction:octanoyl CoA + L carnitine ightleftharpoons CoA + L octanoylcarnitineThus, the two substrates of this enzyme are octanoyl CoA …   Wikipedia

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