Plaque-type porokeratosis

Plaque-type porokeratosis
Plaque-type porokeratosis
Classification and external resources
OMIM 175800
DiseasesDB 32454
MeSH D017499

Plaque-type porokeratosis (also known as "Classic porokeratosis," and "Porokeratosis of Mibelli"[1]) is characterized by skin lesions that start as small, brownish papules that slowly enlarge to form irregular, annular, hyperkeratotic or verrucous plaques.[2]:533[3]:566

See also

Sometimes, they may show gross overgrowth and even horn-like structures may develop.[4] Skin malignancy, although rare is reported from all types of porokeratosis. Squamous cell carcinoma has been reported to develop in Mibelli's type porokeratosis over partianal areas involving anal mucosa. This was the first report mentioning mucosal malignancy in any form of porokeratosis..[5]

References

  1. ^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. pp. 1668. ISBN 1-4160-2999-0. 
  2. ^ Freedberg, et al. (2003). Fitzpatrick's Dermatology in General Medicine. (6th ed.). McGraw-Hill. ISBN 0-07-138076-0.
  3. ^ James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN 0-7216-2921-0.
  4. ^ Familial disseminated plaque type porokeratosis with multiple horns and squamous cell carcinoma involving anal skin
  5. ^ Familial disseminated plaque type porokeratosis with multiple horns and squamous cell carcinoma involving anal skin


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