Guevodoces

Guevodoces is a genetic condition that delays male sexual development until puberty. The affected individual is usually an XY male, but he appears female from birth as a result of delayed testosterone production. At puberty, however, his testes descend and his penis finally develops.

Because of the absence of 5-alpha reductase that is needed to convert testosterone to DHT at birth, genitalia looks female when an individual is born.