Bronchomalacia

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ICD10 = ICD10|Q|32|2|q|30
ICD9 = ICD9|748.3
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Bronchomalacia is a term for weak cartilage in the walls of the bronchial tubes, occurring in children under six months, presented with noisy breathing and/or wheezing. There is collapse of a main stem bronchus, on expiration. There are two types of Bronchomalacia. Primary Bronchomalacia is due to a deficiency in the cartilaginous rings. Secondary Bronchomalacia may occur by extrinsic compression from an enlarged vessel, a vascular ring or a bronchogenic cyst.

Description

Bronchomalacia can best be described as a birth defect of the bronchus in the respiratory tract. Congenital malacia of the large airways is one of the few causes of irreversible airways obstruction in children, with symptoms varying from recurrent wheeze and recurrent lower airways infections to severe dyspnea and respiratory insufficiency. [Carden, KA, Boiselle, PM, Waltz, DA, et al (2005) Tracheomalacia and tracheobronchomalacia in children and adults: an in-depth review. Chest 127,984-1005.] [Clements, B Congenital malformations of the lungs and airways. Taussig, LM Landau, LI eds. Pediatric respiratory medicine 1999,1106-1136 Mosby. St. Louis, MO] [Austin, J, Ali, T Tracheomalacia and bronchomalacia in children: pathophysiology, assessment, treatment and anaesthesia management. Paediatr Anaesth 2003;13,3-11] [McNamara, VM, Crabbe, DC Tracheomalacia. Paediatr Respir Rev 2004;5,147-154]

Classification

*Primary Bronchomalacia
*Secondary Bronchomalacia

Primary Bronchomalacia

* Primary Bronchomalacia is classified as congenital.
* Primary Bronchomalacia is caused by a deficiency in the cartilaginous rings.
* Primary airway malacia was defined as airway malacia in otherwise normal infants. [Benjamin, B Tracheomalacia in infants and children. Ann Otol Rhinol Laryngol 1984;93,438-442]

Secondary Bronchomalacia

* Secondary Bronchomalacia is acquired.
* Secondary Bronchomalacia may occur by extrinsic compression from an enlarged vessel, a vascular ring or a bronchogenic cyst.
* Secondary airway malacia was defined as airway malacia secondary to esophageal atresia, VATER/VACTERL association (condition with vertebral anomalies, anal atresia, congenital heart disease, tracheoesophageal fistula or esophageal atresia, renourinary anomalies, or radial limb defects), vascular or other external compression of the airways, or specific syndromes.

Diagnosis

*Bronchoscopy

Treatment

#Time
##Minimally Invasive, usually in conjunction with Continuous Positive Airflow Pressure.
#Continuous Positive Airflow Pressure
##A method of respiratory ventilation.
#Tracheotomy
##Surgical procedures on the neck to open a direct airway through an incision in the trachea (the windpipe).

Notes

References

*Carden, KA, Boiselle, PM, Waltz, DA, et al (2005) Tracheomalacia and tracheobronchomalacia in children and adults: an in-depth review. Chest 127,984-1005.
*Clements, B Congenital malformations of the lungs and airways. Taussig, LM Landau, LI eds. Pediatric respiratory medicine 1999,1106-1136 Mosby. St. Louis, MO
*Austin, J, Ali, T Tracheomalacia and Bronchomalacia in children: pathophysiology, assessment, treatment and anaesthesia management. Paediatr Anaesth 2003;13,3-11
*McNamara, VM, Crabbe, DC Tracheomalacia. Paediatr Respir Rev 2004;5,147-154
*Benjamin, B Tracheomalacia in infants and children. Ann Otol Rhinol Laryngol 1984;93,438-442

External Links

* [http://www.bronchomalacia.org Bronchomalacia Information and Education]

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name = Congenital malformations and deformations of respiratory system
title = Congenital malformations and deformations of respiratory system (, )
titlestyle = background:Silver
groupstyle = background:MistyRose;

group1 = Nose
list1 = Choanal atresia

group2 = Larynx
list2 = Laryngocele - Laryngomalacia

group3 = Trachea and bronchus
list3 = Tracheomalacia - Bronchomalacia

group4 = Lung
list4 = Bronchiectasis - Pulmonary sequestration - Congenital cystic adenomatoid malformation

group5 =
list6 = "see also (, )"